A case report of atrial flutter and heart failure in patient with Right Ventricular Endomyocardial fibrosis
Keywords:restrictive, cardiomyopathy, warfarin, amiodarone, endocardiectomy, valve replacement.
Endomyocardial fibrosis is a restrictive cardiomyopathy with highest prevalence in Sub-Saharan Africa, usually affecting children and adolescents. The disease usually occurs in a geographical distribution within 15 degrees on either side of equator. Literature shows that most common form is the biventricular endomyocardial fibrosis. This is a report on a 44 years old female patient with recurrent acute heart failure episodes whom diagnosed to have right ventricular endomyocardial fibrosis on Echocardiogram. Her electrocardiogram showed atrial flutter with variable blocks. Currently, she is attending out-patient cardiology clinic and her medications include tablets amiodarone 200mg daiy, warfarin 5mg daily, aldactone 25mg daily, bisoprolol 2.5mg daily and telmisartan 40mg daily. Her International Normalized Ratio (INR) is therapeutic. This case involves the presence of atrial flutter in a patient with right ventricular endomyocardial fibrosis that has not been reported. Also, emphasizes the burden of endomyocardial fibrosis in our local setting, its diagnosis and management.
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